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2 hunters may have died of prion disease from eating contaminated deer meat, researchers say
Researchers have drawn a possible link between the deaths of two hunters in the last couple of years from a rare neurological condition. A report, authored by medical experts from the University of Texas at San Antonio and published earlier this month in the clinical journal Neurology, suggests the men contracted it by consuming venison from deer infected with chronic wasting disease, a degenerative illness not conclusively shown to be transmissible from animals to humans.
Both men hunted at the same lodge and consumed meat from the same deer population before each developed Creutzfeldt-Jakob disease and died soon afterward, the report’s authors said. They did not give the lodge’s specific location. Creutzfeldt-Jakob disease is one of several prion diseases — uncommon neurodegenerative disorders affecting humans that are characterized by an abnormal folding of proteins in the brain, according to the Centers for Disease Control and Prevention. Symptoms broadly mimic those of dementia, although patients afflicted with Creutzfeldt-Jakob deteriorate much more quickly.
The new study centered around the initial death of a 72-year-old man in 2022 who “presented with rapid-onset confusion and aggression,” the authors said. That man apparently had a history of eating meat from a deer population known to be infected with chronic wasting disease. His friend, who had eaten venison from the same deer population, died later from Creutzfeldt-Jakob disease.
The friend’s death came within a month of him developing symptoms typical of the illness, like seizures and agitation, according to the study, and a postmortem ultimately confirmed his diagnosis with a variant form of it called sCJDMM1. Authors said that finding may point to “a possible novel animal-to-human transmission of CWD,” although they acknowledged it did not definitely prove that consuming venison from a deer infected with chronic wasting disease eventually caused Creutzfeldt-Jakob disease in any human being. But that possibility could not be definitively ruled out, either.
“Although causation remains unproven, this cluster emphasizes the need for further investigation into the potential risks of consuming CWD-infected deer and its implications for public health,” they said in the report. CBS News contacted the report’s lead author for comment but did not receive an immediate response.
Prion diseases, including Creutzfeldt-Jakob disease, can have long incubation periods but progress rapidly once symptoms start to present themselves and are always fatal. While they are not well understood, exposure to certain pathogens that then trigger the brain proteins to fold is believed to be the cause.
According to the Mayo Clinic, Creutzfeldt-Jakob disease is thought to emerge in four different ways: sporadically, the most common form, where someone develops the disease without a clear trigger; by inheriting certain genetic changes that cause prion proteins to develop; through contaminated medical instruments used during surgeries or other medical procedures, which is rare; and through consumption of contaminated beef, which is even rarer.
A variant form of Creutzfeldt-Jakob disease has long been tied to eating beef from cattle infected with mad cow disease, or bovine spongiform encephalopathy, which is another prion disorder. The connection between the infections in cattle and humans who ate beef from those cattle gained international attention when it was recognized publicly by government health officials in the United Kingdom in the 1990s, following a string of disease outbreaks.
Even though chronic wasting disease falls, along with mad cow, under the umbrella of prion disorders affecting animals, experts have said no strong evidence exists to indicate that prions seen in chronic wasting disease can infect humans. Some big questions remain about the disease’s transmission across species though, and there have been a few experimental studies that suggest, at least, that chronic wasting disease is transmissible to primates. The CDC writes in a discussion about prion transmission that, however experimental, those studies “raise the concern that CWD may pose a risk to people and suggest that it is important to prevent human exposures to CWD.”
Chronic wasting disease has been reported in free-ranging deer, elk and moose in 32 states across the continental U.S. and four Canadian provinces, as well as in some farmed deer and elk, according to the CDC. The agency has noted that the overall occurrence of the disease nationwide is relatively low, but it can spread quickly through populations where it has been established, and, in the event that it is established, “the risk can remain for a long time in the environment.”
Several hundred deer have tested positive for the disease in Minnesota over the last 20 years or so, mainly in the southeastern part of the state, CBS Minnesota reported. Last year, experts said a captive deer in Wisconsin tested positive for the illness just a few months before officials in Yellowstone National Park announced they had detected the disease in a deer in that area for the first time.
Legislation to expand Social Security benefits to millions of Americans passed the U.S. Senate early Saturday and is now headed to the desk of President Joe Biden, who is expected to sign the measure into law.
Senators voted 76-20 for the Social Security Fairness Act, which would eliminate two federal policies that prevent nearly 3 million people, including police officers, firefighters, postal workers, teachers and others with a public pension, from collecting their full Social Security benefits. The legislation has been decades in the making, as the Senate held its first hearings into the policies in 2003.
“The Senate finally corrects a 50-year mistake,” proclaimed Senate Majority Leader Chuck Schumer, a Democrat from New York, after senators approved the legislation at 12:15 a.m. Saturday.
The bill’s passage is “a monumental victory for millions of public service workers who have been denied the full benefits they’ve rightfully earned,” said Shannon Benton, executive director for the Senior Citizens League, which advocates for retirees and which has long pushed for the expansion of Social Security benefits. “This legislation finally restores fairness to the system and ensures the hard work of teachers, first responders and countless public employees is truly recognized.”
The vote came down to the wire, as the Senate looked to wrap up its current session. Senators rejected four amendments and a budgetary point of order late Friday night that would have derailed the measure, given the small window of time left to pass it.
Vice President-elect JD Vance of Ohio was among the 24 Republican senators to join 49 Democrats to advance the measure in an initial procedural vote that took place Wednesday.
“Social Security is a bedrock of our middle class. You pay into it for 40 quarters, you earned it, it should be there when you retire,” Ohio Senator Sherrod Brown, a Democrat who lost his seat in the November election, told the chamber ahead of Wednesday’s vote. “All these workers are asking for is for what they earned.”
What is the Social Security Fairness Act?
The Social Security Fairness Act would repeal two federal policies — the Windfall Elimination Provision (WEP) and the Government Pension Offset (GPO) — that reduce Social Security payments to nearly 3 million retirees.
That includes those who also collect pensions from state and federal jobs that aren’t covered by Social Security, including teachers, police officers and U.S. postal workers. The bill would also end a second provision that reduces Social Security benefits for those workers’ surviving spouses and family members. The WEP impacts about 2 million Social Security beneficiaries and the GPO nearly 800,000 retirees.
The measure, which passed the House in November, had 62 cosponsors when it was introduced in the Senate last year. Yet the bill’s bipartisan support eroded in recent days, with some Republican lawmakers voicing doubts due to its cost. According to the Congressional Budget Office, the proposed legislation would add a projected $195 billion to federal deficits over a decade.
Without Senate approval, the bill’s fate would have ended with the current session of Congress and would have needed to be re-introduced in the next Congress.
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Saturday is the winter solstice and 2024’s shortest day. Here’s what to know about the official start of winter.
The 2024 winter solstice, the shortest day of the year, happens on Saturday, Dec. 21, in the Northern Hemisphere. The celestial event signifies the first day of winter, astronomically.
What is the winter solstice?
The winter solstice is the day each year that has the shortest period of daylight between sunrise and sunset, and therefore the longest night. It happens when the sun is directly above the Tropic of Capricorn, a line of latitude that circles the globe south of the equator, the National Weather Service explains.
The farther north you are, the shorter the day will be, and in the Arctic Circle, the sun won’t rise at all.
How is the day of the winter solstice determined?
The winter solstice occurs because of the Earth’s tilt as it rotates around the sun.
When the Northern Hemisphere tilts away from the sun, the nights last longer. The longest night happens on the solstice because the hemisphere is in its furthest position from the sun. That occurs each year on Dec. 21 or 22.
This year, it falls on Dec. 21 at 4:21 a.m ET, to be precise.
On the summer solstice, when the northern tilt is closest to the sun, we have the longest day, usually June 20 or 21.
National Weather Service
The solstices are not always exactly on the 21st every year because the earth’s rotation around the sun is 365.25 days, instead of 365 even.
Will days start getting longer after the winter solstice?
Yes. Each day after the solstice, we get one minute more of sunlight. It doesn’t sound like much, but after just two months, or around 60 days, we’ll be seeing about an hour more of sunlight.
When will winter officially be over in 2025?
The meteorological winter ends on March 20, 2025. Then, spring will last until June 20, when the summer solstice arrives.
How is the winter solstice celebrated around the world?
Nations and cultures around the world have celebrated the solstice since ancient times with varying rituals and traditions. The influence of those solstice traditions can still be seen in our celebrations of holidays like Christmas and Hanukkah, Britannica notes.
The ancient Roman Saturnalia festival celebrated the end of the planting season and has close ties with modern-day Christmas. It honored Saturn, the god of harvest and farming. The multiple-day affair had lots of food, games and celebrations. Presents were given to children and the poor, and slaves were allowed to stop working.
Gatherings are held every year at Stonehenge, a monumental circle of massive stones in England that dates back about 5,000 years. The origins of Stonehenge are shrouded in mystery, but it was built to align with the sun on solstice days.
Andrew Matthews/PA Images via Getty Images
The Hopi, a Native American tribe in the northern Arizona area, celebrate the winter solstice with dancing, purification and sometimes gift-giving. A sacred ritual known as the Soyal Ceremony marks the annual milestone.
In Peru, people honor the return of the sun god on the winter solstice. The ancient tradition would be to hold sacrificial ceremonies, but today, people hold mock sacrifices to celebrate. Because Peru is in the Southern Hemisphere, their winter solstice happens in June, when the Northern Hemisphere is marking its summer solstice.
Scandinavia celebrates St. Lucia’s Day, a festival of lights.
The “arrival of winter,” or Dong Zhi, is a Chinese festival where family gathers to celebrate the year so far. Traditional foods include tang yuan, sweet rice balls with a black sesame filling. It’s believed to have its origins in post-harvest celebrations.
Researchers stationed in in Antarctica even have their own traditions, which may include an icy plunge into the polar waters. They celebrate “midwinter” with festive meals, movies and sometimes homemade gifts.